HAE-related laboratory results before starting C1-INH therapies (complement studies for diagnosis must be performed when the patient is not receiving C1-INH replacement therapy, because it will alter results):

 

Normal ranges are shown in parentheses

 

C1q level = 165 mcg/mL     (109-242 mcg/mL)

C3 level = 100 mg/dL     (80-90 mg/dL)

C4 level = 9 mg/dL     (15-45 mg/dL; varies with laboratory)

C1-INH level (C1-INH) level = 3 mg/dL     (16-33 mg/dL)

C1-INH function = 15% of normal     (ELISA assay)